Novosti
Khirurgii
This journal is
indexed in Scopus



Year 2007 Vol. 15 No 4

LECTURES, REVIEWS

SPINDZHUK M.V., ADZERIKHO I.E., DERGACHOV A.V.

ABSTAIN ANOMALY

The definition, history, statistic data, etiology, anatomy and pathophysiology, clinical manifestation, diagnostics and treatment principles of the congenital cyanotic heart disease Abstain anomaly - are briefly described in the article. Treatment tactics of Abstain anomaly is determined by the acuteness degree of the disease itself and influences of accompanying structural and electropathophysiological anomalies. From the medicinal preparations antibiotics are used to prevent infectious endocarditis as well as diuretics, inhibitors of angiotensin converting enzyme and digoxin for the treatment of cardiac insufficiency.
Indications for the surgical treatment are:
1) NYHA class III-VI;
2) significant or progressing cyanosis;
3) reduced tolerance to the physical exercises;
4) significant decrease in the growth graphic curve;
5) acute cardiomegaly (index more than 0, 65);
6) associated cardiac anomalies, including the right ventricle portion obstruction;
7) refractory ventricle and auricle arrhythmias;
8) paradoxical embolism in anamnesis.
Surgical treatment of the anomaly is aimed to prevent intracardiac shunting from the left to the right, to limit cardiomyopathy, to improve tolerance to the physical exercises and functional class. Surgery may be performed in one or more stages.

Keywords: Abstain anomaly, tricuspid insufficiency, congenital heart disease.
p. 112 - 122 of the original issue
References
  1. / . . [ .]. , 1967. 657 .
  2. B. L. Aaron. Congenital tricuspid insufficiency. Definition and review / B. L. Aaron, M. Mills, R. R. Lower // Chest. 1976. N 69. P. 637-641.
  3. Canine tricuspid valve malformation, a model of human Ebstein anomaly, maps to dog chromosome 9 / G. Andelfinger [et al.] // Journal of Medical Genetics. 2003. N 40. P. 320-324.
  4. Pathologic Anatomy of Ebsteins Anomaly of the Heart Revisited / K. R. Anderson, J. T. Lie, K.R. Anderson // The American Journal of Cardiology. 1978. Vol. 41. P. 739-745.
  5. Ebsteins anomaly review of multifaceted congenital cardiac condition / C. H. Jost [et al.] // Swiss Med. WKLY. 2005. N 135. P. 269-281.
  6. Ebsteins anomaly of the tricuspid valve. / E. Bacha [et al.] // UpToDate Patient Information files [Electronic resourse]. Mode of access: Date of access: 15.10.2007.
  7. Mutations in the cardiac transcription factor NKX2.5 affect diverse cardiac developmental pathways. / D. W. Benson [et al] // J. Clin. Invest. 1999. Vol. 104, N 11. P. 1567-1573.
  8. Nelson Pediatric 16 th edition. / A. Castaneda [et al.] [Electronic resourse]. Philadelphia, Saunders, 2000.
  9. Bi-directional cavopulmonary shunt associated with ventriculo and valvuloplasty in Ebsteins anomaly: benefits in high risk patients / S. Chavaud [et al.] // Eur. J. Cardiothorac. Surg. 1998. Vol. 13, N 5. P. 514-519.
  10. Repair of Ebsteins Anomly / S. Chavaud [et al.] // Operative Technique in Thoracic and Vascular Surgery. 2004. Vol.7. N 5. P. 194.207.
  11. Facteurs predictifs de mortalite dans la maladie dEbstein. / D. Crepin [et al.] // Arch. Mal. Coeur. Vaiss. 2004. Vol.97, N 5. 535-539.
  12. Current Cardiology / eds. M. M. Crawford. Appleton Lange, 2002. 600 .
  13. Danielson, K. Surgical repair of Ebsteins anomaly / K. Danielson, K. Gordon, V. K. Fuster, // Ann. Surg. 1982. Vol. 196, N 4. P. 499-504.
  14. Tricuspid Valve Repair for Ebsteins Anomaly / J. Dearani, A. Danielson, K. Gordon // Operative Technique in Thoracic and Vascular Surgery. 2003. Vol. 8, N 4. P. 188-192.
  15. Surgical management of Ebsteins Anomaly in the Adult / J. A. Dearani [et al.] // Semin. Thorac. Cardiovasc. Surg. 2005. N 17. P. 148-154.
  16. Ebsteins Anomaly Associated With an Anomalous Coronary Artery, 2 Myocardial Bridges, and a Mahaim Fiber / J. A. De Lemos [et al] // Circulation. 1999. N 100. P. 1757-1759.
  17. Doty, J. Ebsteins Anomaly / J. Doty // [Electronic resourse]. : http://www.ctsnet.org/residents/ctsn. Date of access: 15.09.2007.
  18. Gates, J. Ebstein Anomaly / J. Gates // [Electronic resourse]. Mode of access:http://www.emedicine.com/cgibin/foxweb.exe/screen@/em/ga?book =radio& authorid = 7193 &topicid=228. Date of access: 15.09.2007.
  19. Evidence-based case report for analgesic and anesthetic management of a parturient with Ebsteins Anomaly and Wolff-parkinson-White syndrome. / V. S. Misa [et al] // International Journal of Obstetric Anesthesia. 2007. N 16. P. 77-81.
  20. Atrioventricular nodal re-entrant tachycardia in a patient with Ebstein anomaly / G. Monning [et al.] // Eur. J. Cardiothorac. Surg. 1998. Vol. 13, N 5. 514-519.
  21. Ebstein-Anomalie: Langzeitverlauf nach Trikuspidal-klappenrekonstruktion ohne Ventrikelplikatur. / N. Nagdyman [et al.] // Z. Kardiol. 2003. P. 730-734.
  22. Plunkett, M. Ebstein Malformation: Surgical Perspective / M. Plunkett, H. Laks // [Electronic resource]. Mode of access: http://www.emedicine. com. Date of access: 15.09.2007.
  23. Riaz, K. Ebstein Anomaly / K. Riaz, A. Forker // [Electronic resource]. Mode of access: http://www.emedicine.com/cgibin/foxweb.exe/screen@/em/ga ?book = med & authorid = 8381 &topicid=627. Date of access: 15.09.2007.
  24. Silva, S. R. Prenatal diagnosis of Downs syndrome in the presence of isolated Ebsteins anomaly. / S. R. Silva, J. P. Bruner, C. A. Moore // Fetal. Diagn. Ther. 1999. Vol. 14, N 3. P. 149-51.
  25. Anomalia de Ebstein / R. S. Silva [et al.] // Arq. Bras. ardiol. 1993. N 4012. P. 133-139.
  26. http://www.mayoclinic.org/ebsteins-anomaly/ [Electronic resourse]. Date of access: 15.10.2007.
  27. Yale Cardiothoracic imaging. Heart Anatomy Electronic Book. [Electronic resource]. Mode of access: http://info.med.yale.edu. Date of access: 15.09.2007.
Contacts | ©Vitebsk State Medical University, 2007