Novosti
Khirurgii

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Year 2019 Vol. 27 No 1

CASE REPORTS

L.A. BOCKERIA, D.K. GUSCHIN, M.M. ZELENIKIN, L.A. YURPOLSKAYA

RARE CASE: FIBROMA OF THE INTERVENTRICULAR SEPTUM IN 17-MONTH-OLD CHILD

A.N. Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow,
The Russian Federation

Frequency of primary heart tumors in children is relatively rare and according to the literature data does not exceed 0.32%, while heart fibroma is registered in 13-18%. Cardiac fibroma is a benign tumor that occurs mainly in childhood. It can be manifested by heart rhythm disturbances, heart failure, sudden death, while large number of patients remain asymptomatic and tumor is revealed accidentally. Electrocardiography and echocardiography help to diagnose this heart neoplasm, but an accurate diagnosis can be made using additional methods such as computer or magnetic resonance imaging and histological examination. Nevertheless, in some situations, nature of tumor can be established only after its resection. This case report describes the stages of diagnosis and subsequent successful resection of a large fibroma of the interventricular septum, which has created the obstruction of right ventricular outflow tract, in a baby patient. It should be noticed that the course of the disease was almost asymptomatic. The tumor was first detected at the age of 1 month when performing routine echocardiography and subsequently the child was observed for several months by cardiologist; there was a tendency to the tumor increase, but there were no specific complaints from the child.

Keywords: child, heart neoplasms, fibroma, interventricular septum, resection
p. 101-107 of the original issue
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Address for correspondence:
121552, The Russian Federation,
Moscow, Rublevskoe Highway, 135,
A.N. Bakoulev National Medical
Research Center for Cardiovascular Surgery,
Surgery Department of Young Children
With Congenital Heart Diseases.
Tel. mobile: +79260310316,
e-mail: medikum@inbox.ru,
Dmitry K. Guschin
Information about the authors:
Bockeria Leo A., Academician of RAS, MD, Professor, Director, A.N. Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation.
http://orcid.org/0000-0002-6180-2619
Guschin Dmitry K., Researcher, Cardiovascular Surgeon of the Surgery Department of Young Children with Congenital Heart Diseases, A.N. Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation.
http://orcid.org/0000-0002-0925-6526
Zelenikin Mikhail M., MD, Professor, Head of the Surgery Department of Young Children with Congenital Heart Diseases, A.N. Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation.
http://orcid.org/0000-0002-1298-2940
Yurpolskaya Lyudmila A., MD, Leading Researcher of the Department of Computer and Magnetic Resonance Imaging, A.N. Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, Russian Federation.
http://orcid.org/0000-0001-7780-2405
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